Report an error   

HERDIN Record #: NCR-PHC-16050618313136 Submitted: 07 May 2016 Modified: 11 May 2016

Isolated Unilateral Pulmonary Artery Agenesis.

See More

Unilateral Pulmonary artery agenesis (UPAA) is a rare congenital anomaly that is frequently associated with other cardiovascular anomalies such as tetralogy of fallot, right aortic arch, septal defects and PDA. Approximately 150 cases of UPAA have been reported. However, since many patients with isolated UPAA have a benign clinical course, the diagnosis may not be made until adulthood when an abnormal chest radiograph initiates a series of diagnostic tests. The patient who survives undetected to adulthood usually presents with an abnormal chest radiograph without concomitant cardiovascular abnormalities. Our purpose is to illustrate that a high index of suspicion is necessary to correctly diagnose these case.

Publication Type
Research Report
LocationLocation CodeAvailable FormatAvailability
Philippine Heart Center Medical Library CR.005.05 Fulltext Print Format

Copyright © One Window Project 2020. All rights reserved.