Sinus of Valsalva aneurysm is a rare cardiac anomaly that is usually undetected until it ruptures. Most aneurysms are single, commonly afflicting the right coronary sinus and when they rupture they commonly drain into the right ventricular outflow tract, often associated with a subarterial type of ventricular septal defect (VSD) with incidence ranging from 20 to 60%. The objectives of this study are, (1) to describe retrospectively the clinical features and laboratory findings of patients diagnosed to have rupture of coronary sinusof Valsalva (RCSOV) and how they were managed and (2) to discuss what the disease is all about. All patients whose diagnosis was RCSOV, and who were admitted from January 1, 2000 to October 20, 2004 in the Philippine Heart Center, were recalled through the Medtrack. Out of the 26 patients who were logged in the computer, only 11 patients charts were retrieved and entered into the registry for congenital heart disease. The clinical features of these patients were described as well as their laboratory and intraoperative findings. This study thoroughly discussed the clinical features of RCSOV patients admitted in the Philippine Heart Center from January 1,2000 to November 20,2004 and gave us insights regarding the disease. It confirmed previous statistics and findings on a relatively rare disease.